자가면역질환과 동반된 후두기관협착 2예

Abstract

Autoimmune disease-associated laryngotracheal stenosis (AD-LTS) is very rare but can pose a life-threatening risk. Pathogenesis of AD-LTS is still uncertain and standard treatment protocol has not been proposed. In this study, we reported two rare cases of AD-LTS in patients with relapsing polychondritis and rheumatoid arthritis, respectively. Two middle-aged female patients visited our clinic due to progressive dyspnea, and stenosis of subglottis and upper trachea was identified. Under general anesthesia, stenotic area was dilated with balloon gradually following steroid injection. As both patients had developed dyspnea after several months postoperatively, they underwent revision surgery. After two times of surgery, dyspnea was relieved and patients are maintaining systemic immunosuppressive therapy with regular rheumatology clinic follow up. AD-LTS should be carefully diagnosed and proper intervention with multidisciplinary team approach is required.